临床与实验病理学杂志
臨床與實驗病理學雜誌
림상여실험병이학잡지
Chinese Journal of Clinical and Experimental Pathology
2015年
10期
1102-1106
,共5页
赵丽%胡晓丽%赵林胜%宋兰云%詹江华
趙麗%鬍曉麗%趙林勝%宋蘭雲%詹江華
조려%호효려%조림성%송란운%첨강화
胆道闭锁%婴儿肝炎综合征%组织病理学评分
膽道閉鎖%嬰兒肝炎綜閤徵%組織病理學評分
담도폐쇄%영인간염종합정%조직병이학평분
biliary atresia%infantile hepatitis syndrome%histopathological assessment grading score
目的:探讨肝组织病理学分级评分在肝外胆道闭锁( biliary atresia, BA)与婴儿肝炎综合征( infantile hepatitis syndrome, IHS)鉴别诊断中的意义。方法收集经活检确诊的34例BA及16例IHS病例,对其进行回顾性分析,重新对胆汁淤积、肝细胞损害、胆管增生、汇管区纤维化、肝细胞及汇管区炎细胞浸润、髓外造血、汇管区水肿、肝细胞巨细胞变等主要的肝组织病理学变化进行分级评分,总分24分。每例依次对上述8个病理学参数进行打分,最后统计总分。结果 BA组及IHS组肝组织病理学总评分差异有统计学意义(P<0.001)。其中胆管增生、汇管区纤维化、汇管区水肿、肝细胞巨细胞变4个病理学参数在BA组及IHS组之间差异有显著性(P<0.001)。结论对BA及IHS主要的肝组织病理学变化进行分级评分有助于二者之间的鉴别诊断。
目的:探討肝組織病理學分級評分在肝外膽道閉鎖( biliary atresia, BA)與嬰兒肝炎綜閤徵( infantile hepatitis syndrome, IHS)鑒彆診斷中的意義。方法收集經活檢確診的34例BA及16例IHS病例,對其進行迴顧性分析,重新對膽汁淤積、肝細胞損害、膽管增生、彙管區纖維化、肝細胞及彙管區炎細胞浸潤、髓外造血、彙管區水腫、肝細胞巨細胞變等主要的肝組織病理學變化進行分級評分,總分24分。每例依次對上述8箇病理學參數進行打分,最後統計總分。結果 BA組及IHS組肝組織病理學總評分差異有統計學意義(P<0.001)。其中膽管增生、彙管區纖維化、彙管區水腫、肝細胞巨細胞變4箇病理學參數在BA組及IHS組之間差異有顯著性(P<0.001)。結論對BA及IHS主要的肝組織病理學變化進行分級評分有助于二者之間的鑒彆診斷。
목적:탐토간조직병이학분급평분재간외담도폐쇄( biliary atresia, BA)여영인간염종합정( infantile hepatitis syndrome, IHS)감별진단중적의의。방법수집경활검학진적34례BA급16례IHS병례,대기진행회고성분석,중신대담즙어적、간세포손해、담관증생、회관구섬유화、간세포급회관구염세포침윤、수외조혈、회관구수종、간세포거세포변등주요적간조직병이학변화진행분급평분,총분24분。매례의차대상술8개병이학삼수진행타분,최후통계총분。결과 BA조급IHS조간조직병이학총평분차이유통계학의의(P<0.001)。기중담관증생、회관구섬유화、회관구수종、간세포거세포변4개병이학삼수재BA조급IHS조지간차이유현저성(P<0.001)。결론대BA급IHS주요적간조직병이학변화진행분급평분유조우이자지간적감별진단。
Purpose To study the values of liver histopathological assessment grading score in differential diagnosis between biliary atresia ( BA) and infantile hepatitis ( IHS) . Methods Thirty four cases of BA and sixteen cases of IHS were analyzed retrospectively, which were diagnosed by biopsy. A hepatic histopathological assessment grading score was developed. This consisted of eight features such as cholestasis, hepatocellular damage, bile duct proliferation, portal edema, portal inflammation, portal fibrosis, extramedullary hemopoiesis and multinucleated giant hepatocytes. The total scores were 24 points. All the cases were assessed one by one. Results The total scores of BA were significantly higher than that of IHS (P<0. 001). The frequencies of bile duct proliferation, portal fibrosis and portal edema were significantly higher in BA than that in IHS group, while the frequency of multinucleated giant hepatocytes was significantly higher in IHS than that in BA group. Conclusions This scoring system is helpful in differentiating BA from IHS.