中国社区医师
中國社區醫師
중국사구의사
Chinese Community Doctors
2014年
19期
117-117,119
,共2页
颅骨锁骨发育不全%X线特征%鉴别诊断
顱骨鎖骨髮育不全%X線特徵%鑒彆診斷
로골쇄골발육불전%X선특정%감별진단
Craneocleidol dysplasia%X-ray characteristics%Differential diagnosis
目的:探讨颅骨锁骨发育不全患者的临床表现及X线特征,以便准确诊断、及时治疗。方法:利用国内数据库检索发表的相关文献报道,纳入资料完整的病例42例,并结合在本院确认3例。结果:颅骨锁骨发育不全国内患病男女比例1.25:1,中位年龄9岁,囟门增大、延迟闭合或不闭合(77.8%)、眼距宽(71.1%)、头围增大、颅面比例失调(66.7%)、牙列不齐(57.8%)是最常见临床表现,囟门迟闭或不闭合(77.8%)、锁骨短小或缺如(75.6%)、颅缝增宽(64.4%)是三大主要X线特征。结论:颅骨锁骨发育不全X线片可确诊,但应与相关疾病鉴别,防止误诊、漏诊。
目的:探討顱骨鎖骨髮育不全患者的臨床錶現及X線特徵,以便準確診斷、及時治療。方法:利用國內數據庫檢索髮錶的相關文獻報道,納入資料完整的病例42例,併結閤在本院確認3例。結果:顱骨鎖骨髮育不全國內患病男女比例1.25:1,中位年齡9歲,囟門增大、延遲閉閤或不閉閤(77.8%)、眼距寬(71.1%)、頭圍增大、顱麵比例失調(66.7%)、牙列不齊(57.8%)是最常見臨床錶現,囟門遲閉或不閉閤(77.8%)、鎖骨短小或缺如(75.6%)、顱縫增寬(64.4%)是三大主要X線特徵。結論:顱骨鎖骨髮育不全X線片可確診,但應與相關疾病鑒彆,防止誤診、漏診。
목적:탐토로골쇄골발육불전환자적림상표현급X선특정,이편준학진단、급시치료。방법:이용국내수거고검색발표적상관문헌보도,납입자료완정적병례42례,병결합재본원학인3례。결과:로골쇄골발육불전국내환병남녀비례1.25:1,중위년령9세,신문증대、연지폐합혹불폐합(77.8%)、안거관(71.1%)、두위증대、로면비례실조(66.7%)、아렬불제(57.8%)시최상견림상표현,신문지폐혹불폐합(77.8%)、쇄골단소혹결여(75.6%)、로봉증관(64.4%)시삼대주요X선특정。결론:로골쇄골발육불전X선편가학진,단응여상관질병감별,방지오진、루진。
Objective:To explore the clinical manifestation and X-ray characteristics of craneocleidol dysplasia,so it can make accurate diagnosis and timely treatment.Methods:Using the related literature reports of domestic database retrieval,combine with 3 cases by our hospital diagnosed,45 effective cases were selected.They were retrospectively summarized and analyzed.Results:Sick men and women proportion of craneocleidol dysplasia in China was 1.25:1.The median age was 9 years old.The most common clinical manifestations were fontanelle increased,delayed closure or no closure(77.8% ),orbital hypertelorism(71.1% ),head circumference increased,craniofacial disproportion(66.7%),irregular dentition(57.8%).The hree main X-ray characteristics were fontanelle closed late or not closed(77.8% ),collar bone short or absent(75.6% ),cranial suture broadening(64.4% ).Conclusion:Craneocleidol dysplasia can be diagnosed by X ray.It should be identified with related diseases,in order to prevent misdiagnosis and missed diagnosis.